Definition And Pathophysiology

  • Visual Axes Of Two Eyes Do Not Meet At Point Of Regard.
  • Motor And Sensory Alignment Of Eyes Lack Synchronization.
  • Child Initially Suffers Diplopia Due To Different Images Presented To Visual Cortex.
  • Brain Suppresses One Image To Eliminate Diplopia.
  • Constant Suppression Causes Amblyopia (Lazy Eye), Leading To Loss Of Binocularity And Stereopsis.

Classification Of Strabismus

Comitant Versus Noncomitant Strabismus

FeatureComitant StrabismusNoncomitant Strabismus
Basic DefectNo Defect In Individual Extraocular Muscles.Extraocular Muscle Paretic, Palsied, Or Restricted.
Ocular MotilityFull Motility In All Positions Of Gaze.Limited In Direction Of Paretic Or Restricted Muscle.
Angle Of DeviationConstant Irrespective Of Direction Or Position Of Gaze.Varies According To Direction Of Gaze.
Common EtiologiesInfantile Esotropia, Accommodative Esotropia, Intermittent Exotropia.Cranial Nerve Palsies, Duane Syndrome, Brown Syndrome.

Types By Direction Of Deviation

  • Esotropia: Inward Or Convergent Deviation.
  • Exotropia: Outward Or Divergent Deviation.
  • Hypertropia: Upward Vertical Deviation.
  • Hypotropia: Downward Vertical Deviation.

Clinical Evaluation

History And General Assessment

  • Note Age Of Onset. Early Detection Essential To Prevent Permanent Visual Impairment.
  • Evaluate Abnormal Head Postures. Face Turns Or Head Tilts Strongly Suggest Diplopia Or Specific Muscle Palsies.

Visual Acuity And Refraction

  • Assess Visual Acuity To Detect Amblyopia.
  • Perform Cycloplegic Refraction And Fundus Evaluation.

Ocular Alignment Tests

Corneal Light Reflex Tests

  • Ideal For Uncooperative Children Or Those With Poor Fixation.
  • Hirschberg Test: Project Light Source Onto Cornea. Asymmetric Reflex Indicates Strabismus.
  • Krimsky Method: Use Prisms Over Eyes To Align Light Reflections. Accurately Measures Degree Of Deviation.

Cover Tests

  • Requires Patient Attention, Good Motility, And Adequate Vision.
  • Cover-Uncover Test: Differentiates Manifest Deviations (Tropias) From Latent Deviations (Phorias).
  • Alternate Cover Test: Rapidly Shift Cover Back And Forth. Identifies Total Deviation Magnitude.

Specific Strabismus Syndromes

Esodeviations

  • Infantile Esotropia: Onset Before Six Months. Characterized By Large Constant Angle And Frequent Cross-Fixation.
  • Accommodative Esotropia: Onset Between Two And Three Years. Uncorrected Hyperopia Drives Excessive Accommodative Convergence.
  • Pseudoesotropia: False Appearance Of Strabismus Due To Flat Nasal Bridge Or Epicanthal Folds. Corneal Light Reflex Remains Centered.

Exodeviations

  • Intermittent Exotropia: Most Common Exodeviation. Outward Drifting During Distance Fixation. Worsens With Fatigue Or Illness.

Cranial Nerve Palsies

  • Third Nerve Palsy: Presents With Exotropia, Hypotropia, And Ptosis.
  • Fourth Nerve Palsy: Presents With Hypertropia. Child Exhibits Head Tilt To Opposite Shoulder.
  • Sixth Nerve Palsy: Presents With Esotropia And Defective Abduction. Head Turned Toward Palsied Muscle.

Management Principles

Non-Surgical Management

  • Amblyopia Therapy: Must Precede Surgical Realignment.
    • Institute Part-Time Or Full-Time Patching (Occlusion) Of Sound Eye.
    • Utilize Penalization Therapy (Atropine Drops Or Fogging Lenses) For Selected Patients.
  • Refractive Correction: Prescribe Spectacles Or Contact Lenses Based On Cycloplegic Refraction.
  • Accommodative Esotropia Management: Prescribe Full Hyperopic Correction To Eliminate Accommodative Effort And Correct Deviation.

Surgical Management

  • Surgical Indications: Restore Ocular Alignment, Maintain Binocular Vision, Eliminate Abnormal Compensatory Head Postures.
  • Infantile Esotropia: Align Eyes Surgically After Successfully Treating Associated Amblyopia.
  • Accommodative Esotropia: Surgery Reserved For Residual Nonaccommodative Component Not Corrected By Glasses.
  • Intermittent Exotropia: Perform Surgery If Deviation Becomes Large Or Increases In Frequency To Prevent Loss Of Binocularity.