Definition And Mechanism

  • Prosthetic device designed to bypass injured organ of Corti.
  • Directly stimulates residual cochlear nerve cells located within spiral ganglion.
  • Converts environmental auditory stimuli into digital radiofrequency impulses.
  • Replaces normal physiologic transmission involving hair cell sound vibration, ion release, and neurotransmitter activation.

Device Components

  • System combines externally worn and surgically implanted internal components.
Component CategorySpecific PartsFunctional Role
ExternalMicrophoneDetects environmental sounds.
ExternalSpeech processorMinicomputer digitizes and codes input signal using proprietary speech processing strategies.
ExternalTransmitter coilRelays coded signals across skin via frequency modulation signal.
InternalReceiverConverts transmitted radiofrequency codes into electrical impulses.
InternalElectrode arrayCreates electrical fields acting directly on cochlear nerve.

Indications And Candidacy

  • Indicated for bilateral severe to profound sensorineural hearing loss exceeding 70 decibels.
  • Requires documented unsatisfactory benefit from conventional hearing aids after 3 to 6 month trial.
  • Minimum age approved by United States Food and Drug Administration reduced to 9 months.
  • Off-label utilization demonstrates efficacy in younger infants and children retaining residual hearing.
  • Early intervention before 2 years of age optimizes outcomes, enabling over 90 percent of children to enter mainstream education.

Preoperative Evaluation

  • Requires comprehensive audiologic testing to establish baseline deficits.
  • High-resolution computed tomography assesses bony temporal bone and inner ear anatomy.
  • Magnetic resonance imaging confirms presence and structural integrity of cochlear nerve.

Surgical Management

  • Procedure performed under general anesthesia.
  • Involves mastoidectomy coupled with widening of facial recess to access inner ear.
  • Internal stimulator package fastened securely within mastoid process.
  • Cochlea opened typically via round window to insert multielectrode array into scala tympani.
  • Extreme caution exercised to prevent cochlear fluid contamination by bone dust or blood.
  • Intraoperative audiologist testing immediately verifies device functional integrity via cranial nerve VIII electrophysiologic responses.
  • Intraoperative plain radiograph confirms precise electrode array placement.

Postoperative Rehabilitation

  • Initial healing period spans 3 to 4 weeks, during which child remains without auditory input.
  • Initial stimulation establishes baseline programming for first sound access.
  • Program modification relies on behavioral testing and observed vocalization changes.
  • Demands intensive, long-term commitment to speech and language therapy.
  • Bilateral implantation preferred over unilateral procedure to improve sound localization and speech understanding in noisy environments.

Complications And Special Considerations

Complication/IssueClinical Management And Prevention
Pneumococcal meningitisRepresents severe potential complication. Strict mandate requires pneumococcal polyvalent vaccine (PCV13) administration prior to surgery.
Acute mastoiditisOccurs in 3.5 percent of implanted children. Successfully managed with intravenous antibiotics, tympanostomy tubes, and abscess drainage without requiring implant removal.
Magnetic resonance imaging incompatibilityStrong magnetic fields risk implant damage. Most modern implants verified safe only for scanners up to 3.0 Tesla.